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| Title : Survival in infants treated with sebelipase Alfa for lysosomal acid lipase deficiency: an open-label, multicenter, dose-escalation study - Jones_2017_Orphanet.J.Rare.Dis_12_25 |
| Author(s) : Jones SA , Rojas-Caro S , Quinn AG , Friedman M , Marulkar S , Ezgu F , Zaki O , Gargus JJ , Hughes J , Plantaz D , Vara R , Eckert S , Arnoux JB , Brassier A , Le Quan Sang KH , Valayannopoulos V |
| Ref : Orphanet J Rare Dis , 12 :25 , 2017 |
| Abstract : Jones_2017_Orphanet.J.Rare.Dis_12_25 |
| ESTHER : Jones_2017_Orphanet.J.Rare.Dis_12_25 |
| PubMedSearch : Jones_2017_Orphanet.J.Rare.Dis_12_25 |
| PubMedID: 28179030 |
| Gene_locus related to this paper: human-LIPA |
| Title : A Phase 3 Trial of Sebelipase Alfa in Lysosomal Acid Lipase Deficiency - Burton_2015_N.Engl.J.Med_373_1010 |
| Author(s) : Burton BK , Balwani M , Feillet F , Baric I , Burrow TA , Camarena Grande C , Coker M , Consuelo-Sanchez A , Deegan P , Di Rocco M , Enns GM , Erbe R , Ezgu F , Ficicioglu C , Furuya KN , Kane J , Laukaitis C , Mengel E , Neilan EG , Nightingale S , Peters H , Scarpa M , Schwab KO , Smolka V , Valayannopoulos V , Wood M , Goodman Z , Yang Y , Eckert S , Rojas-Caro S , Quinn AG |
| Ref : N Engl J Med , 373 :1010 , 2015 |
| Abstract : Burton_2015_N.Engl.J.Med_373_1010 |
| ESTHER : Burton_2015_N.Engl.J.Med_373_1010 |
| PubMedSearch : Burton_2015_N.Engl.J.Med_373_1010 |
| PubMedID: 26352813 |
| Gene_locus related to this paper: human-LIPA |
| Title : Clinical Features of Lysosomal Acid Lipase Deficiency - Burton_2015_J.Pediatr.Gastroenterol.Nutr_61_619 |
| Author(s) : Burton BK , Deegan PB , Enns GM , Guardamagna O , Horslen S , Hovingh GK , Lobritto SJ , Malinova V , McLin VA , Raiman J , Di Rocco M , Santra S , Sharma R , Sykut-Cegielska J , Whitley CB , Eckert S , Valayannopoulos V , Quinn AG |
| Ref : J Pediatr Gastroenterol Nutr , 61 :619 , 2015 |
| Abstract : Burton_2015_J.Pediatr.Gastroenterol.Nutr_61_619 |
| ESTHER : Burton_2015_J.Pediatr.Gastroenterol.Nutr_61_619 |
| PubMedSearch : Burton_2015_J.Pediatr.Gastroenterol.Nutr_61_619 |
| PubMedID: 26252914 |
| Title : Sebelipase alfa over 52 weeks reduces serum transaminases, liver volume and improves serum lipids in patients with lysosomal acid lipase deficiency - Valayannopoulos_2014_J.Hepatol_61_1135 |
| Author(s) : Valayannopoulos V , Malinova V , Honzik T , Balwani M , Breen C , Deegan PB , Enns GM , Jones SA , Kane JP , Stock EO , Tripuraneni R , Eckert S , Schneider E , Hamilton G , Middleton MS , Sirlin C , Kessler B , Bourdon C , Boyadjiev SA , Sharma R , Twelves C , Whitley CB , Quinn AG |
| Ref : Journal of Hepatology , 61 :1135 , 2014 |
| Abstract : Valayannopoulos_2014_J.Hepatol_61_1135 |
| ESTHER : Valayannopoulos_2014_J.Hepatol_61_1135 |
| PubMedSearch : Valayannopoulos_2014_J.Hepatol_61_1135 |
| PubMedID: 24993530 |
| Gene_locus related to this paper: human-LIPA |
| Title : Sequencing and functional annotation of avian pathogenic Escherichia coli serogroup O78 strains reveal the evolution of E. coli lineages pathogenic for poultry via distinct mechanisms - Dziva_2013_Infect.Immun_81_838 |
| Author(s) : Dziva F , Hauser H , Connor TR , van Diemen PM , Prescott G , Langridge GC , Eckert S , Chaudhuri RR , Ewers C , Mellata M , Mukhopadhyay S , Curtiss R, 3rd , Dougan G , Wieler LH , Thomson NR , Pickard DJ , Stevens MP |
| Ref : Infect Immun , 81 :838 , 2013 |
| Abstract : Dziva_2013_Infect.Immun_81_838 |
| ESTHER : Dziva_2013_Infect.Immun_81_838 |
| PubMedSearch : Dziva_2013_Infect.Immun_81_838 |
| PubMedID: 23275093 |
| Gene_locus related to this paper: ecoli-yaim , ecoli-ycfp , ecoli-yqia , ecoli-Z1930 |
| Title : Clinical effect and safety profile of recombinant human lysosomal acid lipase in patients with cholesteryl ester storage disease - Balwani_2013_Hepatology_58_950 |
| Author(s) : Balwani M , Breen C , Enns GM , Deegan PB , Honzik T , Jones S , Kane JP , Malinova V , Sharma R , Stock EO , Valayannopoulos V , Wraith JE , Burg J , Eckert S , Schneider E , Quinn AG |
| Ref : Hepatology , 58 :950 , 2013 |
| Abstract : Balwani_2013_Hepatology_58_950 |
| ESTHER : Balwani_2013_Hepatology_58_950 |
| PubMedSearch : Balwani_2013_Hepatology_58_950 |
| PubMedID: 23348766 |
| Title : Comparison of the oxime-induced reactivation of erythrocyte and muscle acetylcholinesterase following inhibition by sarin or paraoxon, using a perfusion model for the real-time determination of membrane-bound acetylcholinesterase activity - Eckert_2008_Biochem.Pharmacol_75_698 |
| Author(s) : Eckert S , Eyer P , Herkert N , Bumm R , Weber G , Thiermann H , Worek F |
| Ref : Biochemical Pharmacology , 75 :698 , 2008 |
| Abstract : Eckert_2008_Biochem.Pharmacol_75_698 |
| ESTHER : Eckert_2008_Biochem.Pharmacol_75_698 |
| PubMedSearch : Eckert_2008_Biochem.Pharmacol_75_698 |
| PubMedID: 17977518 |
| Title : Effects of oximes on rate of decarbamylation of human red blood cell AChE measured with two different methods - Eckert_2008_Biochem.Pharmacol_75_1561 |
| Author(s) : Eckert S , Eyer P , Melzer M , Thiermann H , Worek F |
| Ref : Biochemical Pharmacology , 75 :1561 , 2008 |
| Abstract : Eckert_2008_Biochem.Pharmacol_75_1561 |
| ESTHER : Eckert_2008_Biochem.Pharmacol_75_1561 |
| PubMedSearch : Eckert_2008_Biochem.Pharmacol_75_1561 |
| PubMedID: 18281016 |
| Title : Identical kinetics of human erythrocyte and muscle acetylcholinesterase with respect to carbamate pre-treatment, residual activity upon soman challenge and spontaneous reactivation after withdrawal of the inhibitors - Herkert_2008_Toxicology_246_188 |
| Author(s) : Herkert NM , Eckert S , Eyer P , Bumm R , Weber G , Thiermann H , Worek F |
| Ref : Toxicology , 246 :188 , 2008 |
| Abstract : Herkert_2008_Toxicology_246_188 |
| ESTHER : Herkert_2008_Toxicology_246_188 |
| PubMedSearch : Herkert_2008_Toxicology_246_188 |
| PubMedID: 18304715 |
| Title : Reversible inhibition of acetylcholinesterase by carbamates or huperzine A increases residual activity of the enzyme upon soman challenge - Eckert_2007_Toxicology_233_180 |
| Author(s) : Eckert S , Eyer P , Worek F |
| Ref : Toxicology , 233 :180 , 2007 |
| Abstract : Eckert_2007_Toxicology_233_180 |
| ESTHER : Eckert_2007_Toxicology_233_180 |
| PubMedSearch : Eckert_2007_Toxicology_233_180 |
| PubMedID: 17097792 |
| Title : Development of antidotes: problems and strategies - Szinicz_2007_Toxicology_233_23 |
| Author(s) : Szinicz L , Worek F , Thiermann H , Kehe K , Eckert S , Eyer P |
| Ref : Toxicology , 233 :23 , 2007 |
| Abstract : Szinicz_2007_Toxicology_233_23 |
| ESTHER : Szinicz_2007_Toxicology_233_23 |
| PubMedSearch : Szinicz_2007_Toxicology_233_23 |
| PubMedID: 16949190 |
| Title : Development of a dynamic model for real-time determination of membrane-bound acetylcholinesterase activity upon perfusion with inhibitors and reactivators - Eckert_2006_Biochem.Pharmacol_72_358 |
| Author(s) : Eckert S , Eyer P , Muckter H , Worek F |
| Ref : Biochemical Pharmacology , 72 :358 , 2006 |
| Abstract : Eckert_2006_Biochem.Pharmacol_72_358 |
| ESTHER : Eckert_2006_Biochem.Pharmacol_72_358 |
| PubMedSearch : Eckert_2006_Biochem.Pharmacol_72_358 |
| PubMedID: 16725113 |
| Title : Kinetic analysis of the protection afforded by reversible inhibitors against irreversible inhibition of acetylcholinesterase by highly toxic organophosphorus compounds - Eckert_2006_Biochem.Pharmacol_72_344 |
| Author(s) : Eckert S , Eyer P , Muckter H , Worek F |
| Ref : Biochemical Pharmacology , 72 :344 , 2006 |
| Abstract : Eckert_2006_Biochem.Pharmacol_72_344 |
| ESTHER : Eckert_2006_Biochem.Pharmacol_72_344 |
| PubMedSearch : Eckert_2006_Biochem.Pharmacol_72_344 |
| PubMedID: 16780806 |